{"id":19185,"date":"2015-01-05T12:02:48","date_gmt":"2015-01-05T11:02:48","guid":{"rendered":"http:\/\/www.invarena.cz\/?p=19185"},"modified":"2015-01-05T12:02:48","modified_gmt":"2015-01-05T11:02:48","slug":"mlada-vedkyne-ziskala-v-soulu-oceneni-za-vyzkum-nove-lecby-wilsonovy-nemoci","status":"publish","type":"post","link":"https:\/\/www.invarena.cz\/?p=19185","title":{"rendered":"Mlad\u00e1 v\u011bdkyn\u011b z\u00edskala v Soulu ocen\u011bn\u00ed za v\u00fdzkum nov\u00e9 l\u00e9\u010dby Wilsonovy nemoci"},"content":{"rendered":"<p><strong>Postgradu\u00e1ln\u00ed studentka 1. l\u00e9ka\u0159sk\u00e9 fakulty Univerzity Karlovy MUDr. Jana Mattov\u00e1 z\u00edskala v korejsk\u00e9m Soulu ocen\u011bn\u00ed za v\u00fdzkum, kter\u00fd se zab\u00fdv\u00e1 nov\u00fdmi mo\u017enosti l\u00e9\u010dby Wilsonovy nemoci \u2013 tedy genetick\u00e9 poruchy, kter\u00e1 nedovol\u00ed organismu spr\u00e1vn\u011b vylu\u010dovat m\u011b\u010f.<\/strong><!--more--><\/p>\n<p>Cenu obdr\u017eela na sv\u011btov\u00e9m kongresu intern\u00ed medic\u00edny, kde byla jej\u00ed pr\u00e1ce ocen\u011bna ze 130 000 p\u0159ihl\u00e1\u0161en\u00fdch s dal\u0161\u00edmi 24 abstrakty Cestovatelsk\u00fdm grantem.<\/p>\n<p>Vrozen\u00e1 genetick\u00e1 porucha zp\u016fsobuje, \u017ee se m\u011b\u010f p\u0159ijat\u00e1 v potrav\u011b nedostate\u010dn\u011b vylu\u010duje a ukl\u00e1d\u00e1 se v j\u00e1trech a \u010d\u00e1ste\u010dn\u011b i v mozku posti\u017een\u00e9ho. J\u00e1tra tak nemohou spr\u00e1vn\u011b fungovat, a pokud se choroba nel\u00e9\u010d\u00ed, posti\u017een\u00e9mu hroz\u00ed \u00famrt\u00ed v d\u016fsledku selh\u00e1n\u00ed jater. Nahromad\u011bn\u00ed tohoto kovu v mozku je p\u0159\u00ed\u010dinou motorick\u00fdch \u010di psychiatrick\u00fdch poruch. &#8222;Dnes sice existuj\u00ed l\u00e9ky, kter\u00e9 um\u00ed zachytit m\u011b\u010f, ale krom\u011b n\u00ed zadr\u017euj\u00ed i \u017eelezo, zinek a dal\u0161\u00ed kovy, co\u017e nen\u00ed pro pacienta p\u0159\u00edzniv\u00e9,&#8220; vysv\u011btlila MUDr. Mattov\u00e1. Nemocn\u00fd m\u016f\u017ee toti\u017e v d\u016fsledku nedostatku pot\u0159ebn\u00fdch kov\u016f trp\u011bt chudokrevnost\u00ed, sn\u00ed\u017een\u00edm imunity i dal\u0161\u00edmi zdravotn\u00edmi probl\u00e9my.<\/p>\n<p>MUDr. Mattov\u00e9 se d\u00edky v\u00fdzkumu na laboratorn\u00edch potkanech poda\u0159ilo ov\u011b\u0159it t\u0159i vhodn\u00e9 ligandy. &#8222;Ve v\u00fdsledku jsme pozorovali, \u017ee ka\u017ed\u00fd z nich byl schopn\u00fd sn\u00ed\u017eit obsah m\u011bdi ve vybran\u00fdch org\u00e1nech zv\u00ed\u0159ete,&#8220; vysv\u011btlila. Doplnila, \u017ee chemick\u00e9 slo\u017een\u00ed experiment\u00e1ln\u00edch l\u00e1tek navrhl Mgr. Martin Hrub\u00fd, Ph.D., z \u00dastavu makromolekul\u00e1rn\u00ed chemie Akademie v\u011bd \u010cR. Prim\u00e1rn\u00edm c\u00edlem v\u00fdzkumn\u00edk\u016f je dos\u00e1hnout toho, aby se nalezen\u00e9 slou\u010deniny mohly v budoucnu st\u00e1t potravinov\u00fdm dopl\u0148kem a ide\u00e1ln\u011b pozd\u011bji i schv\u00e1len\u00fdm l\u00e9\u010divem pro l\u00e9\u010dbu Wilsonovy nemoci.<\/p>\n<p>Wilsonovou chorobou trp\u00ed na cel\u00e9m sv\u011bt\u011b jeden \u010dlov\u011bk z 30 000. Mnohem v\u00edce je v\u0161ak nositel\u016f genu pro tuto vrozenou poruchu, u nich\u017e se ale nemoc nijak neprojevuje &#8211; je to p\u0159ibli\u017en\u011b jeden \u010dlov\u011bk z 90. Pokud se v\u0161ak stane, \u017ee dva nositel\u00e9 genu spolu zplod\u00ed potomka, je v\u00edc ne\u017e pravd\u011bpodobn\u00e9, \u017ee u n\u011bj nemoc propukne. V Evrop\u011b je choroba roz\u0161\u00ed\u0159en\u00e1 hlavn\u011b ve v\u00fdchodn\u00edch st\u00e1tech a v It\u00e1lii. V \u010cesku je o n\u011bco m\u00e9n\u011b \u010dast\u00e1.<\/p>\n<p>Parlamentn\u00ed listy<\/p>\n","protected":false},"excerpt":{"rendered":"<div class=\"mh-excerpt\"><p>Postgradu\u00e1ln\u00ed studentka 1. l\u00e9ka\u0159sk\u00e9 fakulty Univerzity Karlovy MUDr. Jana Mattov\u00e1 z\u00edskala v korejsk\u00e9m Soulu ocen\u011bn\u00ed za v\u00fdzkum, kter\u00fd se zab\u00fdv\u00e1 nov\u00fdmi mo\u017enosti l\u00e9\u010dby Wilsonovy nemoci <a class=\"mh-excerpt-more\" href=\"https:\/\/www.invarena.cz\/?p=19185\" title=\"Mlad\u00e1 v\u011bdkyn\u011b z\u00edskala v Soulu ocen\u011bn\u00ed za v\u00fdzkum nov\u00e9 l\u00e9\u010dby Wilsonovy nemoci\">[&#8230;]<\/a><\/p>\n<\/div>","protected":false},"author":1,"featured_media":14127,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[9],"tags":[],"class_list":["post-19185","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-zpravy"],"_links":{"self":[{"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/posts\/19185","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=19185"}],"version-history":[{"count":0,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/posts\/19185\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/media\/14127"}],"wp:attachment":[{"href":"https:\/\/www.invarena.cz\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=19185"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=%2Fwp%2Fv2%2Fcategories&post=19185"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=%2Fwp%2Fv2%2Ftags&post=19185"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}