{"id":21271,"date":"2015-05-13T08:49:23","date_gmt":"2015-05-13T06:49:23","guid":{"rendered":"http:\/\/www.invarena.cz\/?p=21271"},"modified":"2015-05-13T08:49:23","modified_gmt":"2015-05-13T06:49:23","slug":"bmxmtb-charity-jam-podpori-ctyri-deti-s-nelecitelnou-nemoci","status":"publish","type":"post","link":"https:\/\/www.invarena.cz\/?p=21271","title":{"rendered":"BMX\/MTB Charity Jam podpo\u0159\u00ed \u010dty\u0159i d\u011bti s nel\u00e9\u010ditelnou nemoc\u00ed"},"content":{"rendered":"<p><strong>Lo\u0148sk\u00fd ro\u010dn\u00edk cyklistick\u00e9ho z\u00e1vodu BMX\/MTB Charity Jam organiz\u00e1tory ze sportovn\u00edho klubu Demons Bike p\u0159ekvapil. Nemocn\u00e9 Emmi\u010dce Kopt\u00e1kov\u00e9, na jej\u00ed\u017e podporu sout\u011b\u017e uspo\u0159\u00e1dali, mohli p\u0159edat \u0161ek na 54 050 korun. D\u00edky sponzor\u016fm, partner\u016fm, ale hlavn\u011b obyvatel\u016fm Brumova-Bylnice, kte\u0159\u00ed na akci p\u0159i\u0161li a p\u0159isp\u011bli.<\/strong><!--more--><\/p>\n<p>Brumov-Bylnice \u2013 Letos se chyst\u00e1 Demons Bike pomoci hned \u010dty\u0159em d\u011btem z kraje, kter\u00e9 trp\u00ed nevyl\u00e9\u010ditelnou chorobou a jejich\u017e l\u00e9\u010dba je drah\u00e1. \u0160est\u00fd ro\u010dn\u00edk BMX\/MTB Charity Jam se chyst\u00e1 na 11. \u010dervence v are\u00e1lu b\u00fdval\u00e9ho koupali\u0161t\u011b v Brumov\u011b-Bylnici.<\/p>\n<p>Finan\u010dn\u00ed v\u00fdt\u011b\u017eek m\u00e1 tentokr\u00e1t pomoci sestr\u00e1m \u0160abov\u00fdm z Pozlovic. Jedenap\u016fllet\u00e1 M\u00ed\u0161a i t\u0159\u00edlet\u00e1 Karol\u00ednka maj\u00ed nemoc zvanou mukopolysacharid\u00f3za (MPS) t\u0159et\u00edho stupn\u011b. Jedn\u00e1 se o velmi vz\u00e1cn\u00e9, geneticky podm\u00edn\u011bn\u00e9 onemocn\u011bn\u00ed. Hol\u010di\u010dk\u00e1m chyb\u00ed \u017eivotn\u011b d\u016fle\u017eit\u00fd enzym v bu\u0148k\u00e1ch, organismus proto nen\u00ed schopn\u00fd odbour\u00e1vat mukopolysacharidy, kter\u00e9 jsou p\u0159\u00edtomny v t\u011ble ka\u017ed\u00e9ho z n\u00e1s. Ty se pak hromad\u00ed a usazuj\u00ed v bu\u0148k\u00e1ch \u017eivotn\u011b d\u016fle\u017eit\u00fdch org\u00e1n\u016f \u2013 v j\u00e1trech, slezin\u011b, srdci nebo mozku. Napaden\u00e9 org\u00e1ny postupn\u011b omezuj\u00ed svoji funkci a\u017e do \u00fapln\u00e9ho selh\u00e1n\u00ed.<\/p>\n<p>&#8222;Je to finan\u010dn\u011b n\u00e1ro\u010dn\u00e1 nemoc. Rodina \u0160abov\u00fdch je v t\u011b\u017ek\u00e9 soci\u00e1ln\u00ed situaci. Star\u00e1 se je\u0161t\u011b o t\u0159et\u00ed d\u00edt\u011b, sedmilet\u00e9ho zdrav\u00e9ho Ondru. Proto bychom cht\u011bli pomoci pr\u00e1v\u011b jim,&#8220; \u0159\u00edkaj\u00ed organiz\u00e1to\u0159i.<\/p>\n<p>Vzhledem k vysok\u00e9 \u00fasp\u011b\u0161nosti p\u0159edchoz\u00edho ro\u010dn\u00edku se v\u0161ak rozhodli, \u017ee leto\u0161n\u00ed ro\u010dn\u00edk Charity Jam podpo\u0159\u00ed tak\u00e9 p\u011btadvacetiletou M\u00ed\u0161u a dvaadvacetilet\u00e9ho Davida. Michaela Matulov\u00e1 poch\u00e1z\u00ed z Brumova-Bylnice a m\u00e1 kombinovanou vadu \u2013 t\u011b\u017ek\u00e9 ment\u00e1ln\u00ed a t\u011blesn\u00e9 posti\u017een\u00ed. David Fibichr z Horn\u00edho N\u011bm\u010d\u00ed u\u017e v\u00edce ne\u017e dvacet let bojuje s nemoc\u00ed mot\u00fdl\u00edch k\u0159\u00eddel. Tato nemoc se projevuje velmi zranitelnou k\u016f\u017e\u00ed a tvorbou bolestiv\u00fdch puch\u00fd\u0159\u016f po cel\u00e9m t\u011ble. Onemocn\u011bn\u00ed postihuje tak\u00e9 tr\u00e1vic\u00ed trakt, d\u00fdchac\u00ed \u00fastroj\u00ed, sliznici a vylu\u010dovac\u00ed \u00fastroj\u00ed.<\/p>\n<p>Akce m\u00e1 ka\u017edoro\u010dn\u011b m\u00edstn\u00ed sponzory, kte\u0159\u00ed finan\u010dn\u011b p\u0159ip\u00edvaj\u00ed. Do kone\u010dn\u00e9 sumy, kter\u00e1 bude v den z\u00e1vod\u016f p\u0159ed\u00e1na rodi\u010d\u016fm d\u011bt\u00ed, se zapo\u010d\u00edt\u00e1v\u00e1 tak\u00e9 dobrovoln\u00e9 vstupn\u00e9, p\u0159\u00edsp\u011bvky p\u0159es bankovn\u00ed konto a v\u00fdt\u011b\u017eek z propaga\u010dn\u00edch p\u0159edm\u011bt\u016f, kter\u00fdmi jsou n\u00e1ramky \u010di tri\u010dka, je\u017e je mo\u017en\u00e9 zakoupit na m\u00edst\u011b.<\/p>\n<p>BMX\/MTB Charity Jam je tradi\u010dn\u011b pod z\u00e1\u0161titou m\u00edstostarosty V\u00e1clava Bli\u017e\u0148\u00e1ka, kter\u00fd dohl\u00ed\u017e\u00ed na finan\u010dn\u00ed transakce.<\/p>\n<p>&#8222;\u00da\u010dast potvrdily \u0161pi\u010dky BMX a MTB sc\u00e9ny v\u010detn\u011b Michaela Berana, kter\u00fd se na sv\u00e9m kole v m\u00edstn\u00edm parku proh\u00e1n\u011bl u\u017e v p\u0159edchoz\u00edm ro\u010dn\u00edku. V\u0161ichni jezdci i organiz\u00e1to\u0159i se vzdali finan\u010dn\u00edch odm\u011bn ve prosp\u011bch M\u00ed\u0161i a K\u00e1ji, Michaely a Davida,&#8220; dod\u00e1vaj\u00ed organiz\u00e1to\u0159i.<\/p>\n<p>Pomoci mohou v\u0161ichni 212348578\/600<\/p>\n<p>Zl\u00ednsk\u00fd den\u00edk<br \/>\n<a href=\"http:\/\/www.zlinsky.denik.cz\/\">http:\/\/www.zlinsky.denik.cz\/<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<div class=\"mh-excerpt\"><p>Lo\u0148sk\u00fd ro\u010dn\u00edk cyklistick\u00e9ho z\u00e1vodu BMX\/MTB Charity Jam organiz\u00e1tory ze sportovn\u00edho klubu Demons Bike p\u0159ekvapil. Nemocn\u00e9 Emmi\u010dce Kopt\u00e1kov\u00e9, na jej\u00ed\u017e podporu sout\u011b\u017e uspo\u0159\u00e1dali, mohli p\u0159edat \u0161ek <a class=\"mh-excerpt-more\" href=\"https:\/\/www.invarena.cz\/?p=21271\" title=\"BMX\/MTB Charity Jam podpo\u0159\u00ed \u010dty\u0159i d\u011bti s nel\u00e9\u010ditelnou nemoc\u00ed\">[&#8230;]<\/a><\/p>\n<\/div>","protected":false},"author":1,"featured_media":19889,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[9],"tags":[],"class_list":["post-21271","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-zpravy"],"_links":{"self":[{"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/posts\/21271","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=21271"}],"version-history":[{"count":0,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/posts\/21271\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=\/wp\/v2\/media\/19889"}],"wp:attachment":[{"href":"https:\/\/www.invarena.cz\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=21271"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=%2Fwp%2Fv2%2Fcategories&post=21271"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.invarena.cz\/index.php?rest_route=%2Fwp%2Fv2%2Ftags&post=21271"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}